Li Youjun, Lu Jie, Prochownik Edward V
Children's Hospital of Pittsburgh, Department of Molecular Genetics and Biochemistry, University of Pittsburgh Medical Center, and University of Pittsburgh Cancer Institute, University of Pittsburgh, Pittsburgh, PA 15213, USA.
Proc Natl Acad Sci U S A. 2007 Feb 27;104(9):3490-5. doi: 10.1073/pnas.0610163104. Epub 2007 Feb 20.
Genomic instability (GI) is essential for the initiation and evolution of many cancers and often precedes frank neoplastic conversion. Although GI can occur at several levels, the most conspicuous examples involve gains or losses of entire chromosomes (aneuploidy), the antecedent of which may be whole genome duplication (tetraploidy). Through largely undefined mechanisms, the c-Myc oncoprotein and its downstream target, MTMC1, promote tetraploidy and other forms of GI. In myeloid cells, c-Myc and MTMC1 also regulate a common, small subset of c-Myc target genes including GP1Balpha, which encodes a subunit of the von Willebrand's factor receptor complex that mediates platelet adhesion and aggregation. Gp1balpha also participates in megakaryocyte endomitosis, a form of controlled and precise whole-genome amplification. In this article, we show that both c-Myc and MTMC1 strongly up-regulate Gp1balpha concurrent with their promotion of tetraploidy. shRNA-mediated inhibition of Gp1balpha prevents tetraploidy by both c-Myc and MTMC1, whereas Gp1balpha overexpression alone is sufficient to induce tetraploidy in established and primary cells. Once acquired, tetraploidy persists in most cases examined. Our results indicate that chromosome-level GI, induced by c-Myc overexpression, proceeds by means of the sequential up-regulation of MTMC1 and Gp1balpha and further suggest that the pathways leading to megakaryocytic endomitosis and c-Myc-induced tetraploidy are mechanistically linked by their reliance on Gp1balpha.
基因组不稳定(GI)对于许多癌症的起始和演变至关重要,并且通常先于明显的肿瘤转化。尽管GI可在多个层面发生,但最显著的例子涉及整条染色体的增减(非整倍体),其前身可能是全基因组复制(四倍体)。通过 largely 未明确的机制,c-Myc 癌蛋白及其下游靶点 MTMC1 促进四倍体和其他形式的 GI。在髓系细胞中,c-Myc 和 MTMC1 还调节 c-Myc 靶基因的一个共同的小亚群,包括 GP1Bα,它编码血管性血友病因子受体复合物的一个亚基,介导血小板黏附和聚集。Gp1balpha 也参与巨核细胞内复制,这是一种受控且精确的全基因组扩增形式。在本文中,我们表明 c-Myc 和 MTMC1 在促进四倍体的同时强烈上调 Gp1balpha。shRNA 介导的 Gp1balpha 抑制可阻止 c-Myc 和 MTMC1 诱导的四倍体,而单独的 Gp1balpha 过表达足以在已建立的细胞和原代细胞中诱导四倍体。一旦获得,四倍体在大多数检测的情况下会持续存在。我们的结果表明,由 c-Myc 过表达诱导的染色体水平的 GI 通过 MTMC1 和 Gp1balpha 的顺序上调而发生,并且进一步表明导致巨核细胞内复制和 c-Myc 诱导的四倍体的途径在机制上通过它们对 Gp1balpha 的依赖而联系在一起。