一名患有高同型半胱氨酸血症的成年患者的动脉粥样硬化性烟雾病。

Atherosclerotic adult Moya-Moya disease in a patient with hyperhomocysteinaemia.

作者信息

Cerrato P, Grasso M, Lentini A, Destefanis E, Bosco G, Caprioli M, Bradac G B, Bergui M

机构信息

Department of Neuroscience, University of Turin, Via Cherasco 15, I-10126 Turin, Italy.

出版信息

Neurol Sci. 2007 Mar;28(1):45-7. doi: 10.1007/s10072-007-0748-6.

DOI:10.1007/s10072-007-0748-6

PMID:17385096

Abstract

Moya-Moya is a rare cerebrovascular occlusive disease characterized by bilateral stenosis or occlusion at the terminal portion of the internal carotid artery and abnormal vascular network at the base of the brain, named "moya-moya". In children, Moya-Moya disease usually presents with ischemic cerebrovascular events, mainly TIA or lacunar stroke, leading to mental deterioration. In adults, especially in females, it presents with intracranial haemorrhages. We describe the case of an adult patient with an atherosclerotic Moya-Moya disease which presented with a cerebral borderzone infarction.

摘要

烟雾病是一种罕见的脑血管闭塞性疾病，其特征为双侧颈内动脉末端狭窄或闭塞以及脑底部异常血管网，即“烟雾状血管”。在儿童中，烟雾病通常表现为缺血性脑血管事件，主要是短暂性脑缺血发作（TIA）或腔隙性卒中，导致智力衰退。在成人中，尤其是女性，其表现为颅内出血。我们描述了一例患有动脉粥样硬化性烟雾病并出现脑分水岭梗死的成年患者的病例。