Ahmed R, Ahsan H
Liaquat National Hospital, Karachi.
J Pak Med Assoc. 1997 Jul;47(7):181-5.
Moya Moya disease is a rare disease causing occlusion of the supraclinoid portions of the internal carotid arteries. The CT, MRI and Angiography findings of four patients of Moya Moya disease are presented. CT revealed presence of infarction in the bilateral cerebral hemispheres and atrophy in all patients who had CT. CT was also able to detect abnormal vessels at basal ganglia in one patient. MRI was more informative and besides showing the infarctions and atrophy it also revealed abnormal Moya Moya vessels in all patients. Cerebral angiography is the most definitive method of diagnosis. It showed occlusion of supra clinoid portion of internal carotid arteries on both sides in three patients and on one side in one patient. It also showed pressure of Moya Moya vessels in all cases. It also showed collaterals from meningeal and ophthalmic arteries in all cases. Imaging findings of Moya Moya disease are very specific and provide early diagnosis.
烟雾病是一种导致颈内动脉床突上段闭塞的罕见疾病。本文介绍了4例烟雾病患者的CT、MRI和血管造影检查结果。CT显示所有接受CT检查的患者双侧大脑半球均存在梗死及萎缩。CT还在1例患者中检测到基底节区的异常血管。MRI提供的信息更多，除了显示梗死和萎缩外，还在所有患者中发现了异常的烟雾血管。脑血管造影是最具确诊性的诊断方法。它显示3例患者双侧颈内动脉床突上段闭塞，1例患者单侧闭塞。它还在所有病例中显示了烟雾血管的情况。它还在所有病例中显示了来自脑膜动脉和眼动脉的侧支循环。烟雾病的影像学表现非常具有特异性，可实现早期诊断。
