Gávai M, Hupuczi P, Berkes E, Beke A, Hruby E, Murber A, Urbancsek J, Papp Z
I. Department of Obstetrics and Gynecology, Semmelweis University, Budapest, Hungary.
Int J Obstet Anesth. 2007 Jul;16(3):284-7. doi: 10.1016/j.ijoa.2006.11.014. Epub 2007 Apr 3.
Kartagener's syndrome is an inherited disease characterized by a triad of symptoms: bronchiectasis, situs inversus and sinusitis resulting from defective cilial motility. There are few reports in the literature regarding the optimum anesthetic technique in patients with Kartagener's syndrome. The main anesthetic considerations are related to the respiratory system and increased risk of infection. We report the case of a woman with Kartagener's syndrome and a twin pregnancy conceived by in-vitro fertilization-embryo transfer, who underwent cesarean section under spinal anesthesia. Despite recurrent pulmonary problems, the twin pregnancy resulted in a successful outcome. This was facilitated by a close working relationship between the obstetrician, anesthesiologist and patient.
卡塔格内综合征是一种遗传性疾病,其特征为三联征症状:支气管扩张、内脏转位和由于纤毛运动功能缺陷导致的鼻窦炎。关于卡塔格内综合征患者的最佳麻醉技术,文献报道较少。主要的麻醉考虑因素与呼吸系统及感染风险增加有关。我们报告一例患有卡塔格内综合征且通过体外受精 - 胚胎移植受孕的双胎妊娠女性病例,该患者在蛛网膜下腔麻醉下行剖宫产术。尽管存在反复的肺部问题,但双胎妊娠仍获得成功结局。产科医生、麻醉医生和患者之间密切的合作关系促进了这一结果。