Inoue Yoshimasa, Suga Atsushi, Sekido Yasutomo, Yamada Shunsuke, Iwazaki Masayuki
Department of General Thoracic Surgery, Tokai University Hachioji Hospital, Japan.
Tokai J Exp Clin Med. 2011 Jul 20;36(2):21-4.
Kartagener's syndrome is a rare inherited disorder with a triology of symptoms (bronchiectasis, sinusitis and situs inversus) and is also associated with abnormalities of the cilia of the respiratory epithelium. Lung cancer arising in Kartagener's syndrome is very rare and to date only 5 cases have been reported in the English and Japanese literature. We report on a case of a 65-year-old Japanese male Kartagener's syndrome patient with squamous cell carcinoma of the lung. A left pneumonectomy was performed and no recurrence was found within 2 years.
卡塔格内综合征是一种罕见的遗传性疾病，具有三联征症状（支气管扩张、鼻窦炎和内脏转位），还与呼吸道上皮纤毛异常有关。卡塔格内综合征患者发生肺癌非常罕见，迄今为止，英文和日文文献中仅报道过5例。我们报告一例65岁日本男性卡塔格内综合征患者发生肺鳞状细胞癌的病例。患者接受了左肺切除术，两年内未发现复发。
