努南综合征患者的小肠粪石：一例报告
Small bowel bezoar in a patient with Noonan syndrome: report of a case.
作者信息
Bitton Asaf, Keagle Jennifer N, Varma Madhulika G
机构信息
Department of Medicine, Brigham and Women's Hospital, Boston, Massachusetts, USA.
出版信息
MedGenMed. 2007 Feb 21;9(1):34.
BACKGROUND AND AIMS
Bezoars occur most commonly in patients with impaired gastrointestinal motility or a history of gastric surgery. Noonan syndrome is associated with gastrointestinal dysfunction and feeding difficulties in children. We report the case of a 64-year-old man with Noonan syndrome who was admitted to the hospital with a small bowel obstruction. An emergency laparotomy was performed and the patient was found to have a phytobezoar of the ileum that had caused edema of the intestinal wall resulting in the obstruction.
METHODS/RESULTS: A review of the literature was performed with PubMed using the keywords "Noonan syndrome, " "bezoars, " and "phytobezoar. " Although problems with gastrointestinal motility in Noonan syndrome appear to improve with age, it is conceivable that in this case, abnormal gastrointestinal motility may have predisposed the patient to this condition.
CONCLUSION
Bezoars are an uncommon but notable cause of small bowel obstruction. This is the first case of a bezoar in a patient with Noonan syndrome reported in the English literature.
背景与目的
胃石最常见于胃肠动力受损或有胃手术史的患者。努南综合征与儿童胃肠功能障碍及喂养困难有关。我们报告一例64岁患有努南综合征的男性患者，因小肠梗阻入院。进行了急诊剖腹手术，发现患者回肠有植物性胃石，导致肠壁水肿进而引起梗阻。
方法/结果：使用关键词“努南综合征”“胃石”和“植物性胃石”在PubMed上进行了文献回顾。尽管努南综合征患者的胃肠动力问题似乎会随着年龄增长而改善，但可以想象，在这种情况下，异常的胃肠动力可能使患者易患此病。
结论
胃石是小肠梗阻的一种罕见但值得注意的病因。这是英文文献中报道的首例努南综合征患者发生胃石的病例。
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