Ilina Maria V, Jaeggi Edgar T, Lee Kyong-Jin
Division of Cardiology, Department of Pediatrics, The Hospital for Sick Children, University of Toronto School of Medicine, Toronto, Ontario, Canada.
Catheter Cardiovasc Interv. 2007 May 1;69(6):881-5. doi: 10.1002/ccd.21064.
We describe an infant with the antenatal diagnosis of a large intracardiac rhabdomyoma causing tricuspid inflow obstruction. Postnatal cyanosis and arterial hypoxemia prompted commencement of intravenous prostaglandin E1 with immediate improvement in saturations. Clinical and genetic testing confirmed diagnosis of tuberous sclerosis. To secure ductal patency, two tandem coronary stents were implanted via an antegrade approach. Several episodes of long RP atrio-ventricular re-entrant tachycardia were observed. At 7(1/2) months of age, the tumor was no longer obstructive to tricuspid inflow, ductal flow was highly restrictive and there was no recurrence of supraventricular tachycardia.
我们描述了一名产前诊断为大型心脏内横纹肌瘤导致三尖瓣流入道梗阻的婴儿。出生后出现的青紫和动脉低氧血症促使开始静脉输注前列腺素E1，饱和度立即得到改善。临床和基因检测确诊为结节性硬化症。为确保动脉导管通畅，通过顺行途径植入了两个串联的冠状动脉支架。观察到几次长RP房室折返性心动过速发作。在7个半月大时，肿瘤不再阻塞三尖瓣流入道，动脉导管血流受到高度限制，室上性心动过速未复发。
