Islam Mohammed N, Bhattacharyya Indraneel, Ojha Junu, Bober Karen, Cohen Donald M, Green James G
Department of Oral and Maxillofacial Pathology, College of Dentistry University of Florida, Gainesville, FL 32610, USA.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2007 Oct;104(4):501-9. doi: 10.1016/j.tripleo.2006.11.053. Epub 2007 Apr 20.
Hemifacial hypertrophy (HFH) is rare and characterized by unilateral enlargement of the head and teeth. Hemifacial hypertrophy is classified as true HFH (THFH) with unilateral enlargement of the viscerocranium, and partial HFH (PHFH) in which not all structures are enlarged. We present a case of THFH and compare and contrast it with a case of PHFH. Hemifacial hypertrophy may cover a wide spectrum of defects or may involve only muscle or bone. Myohyperplasia, reported previously as a separate syndrome, may actually represent a forme fruste of PHFH or THFH. The PHFH patient lead a healthy, normal life without significant psychosocial problems and was reluctant to accept his deformity. Contrastingly, the THFH patient had significant social stigma and compromised health together with major aesthetic morbidity. Treatment planning in THFH is arduous and involves multiple modalities. Therefore, it is imperative to differentiate THFH and PHFH for better understanding and management of the condition.
半侧颜面肥大(HFH)较为罕见,其特征为头部和牙齿的单侧增大。半侧颜面肥大分为真性半侧颜面肥大(THFH),即面颅骨单侧增大,以及部分性半侧颜面肥大(PHFH),其中并非所有结构都会增大。我们报告一例THFH病例,并将其与一例PHFH病例进行比较和对比。半侧颜面肥大可能涵盖广泛的缺陷,或者可能仅涉及肌肉或骨骼。先前报道为一种单独综合征的肌增生,实际上可能是PHFH或THFH的一种顿挫型。PHFH患者过着健康、正常的生活,没有明显的心理社会问题,并且不愿接受自己的畸形。相比之下,THFH患者有明显的社会耻辱感,健康受损,同时存在严重的美学问题。THFH的治疗规划艰巨,涉及多种方式。因此,为了更好地理解和管理这种疾病,区分THFH和PHFH至关重要。