Patil K, Mahima V G, Shetty S K, Lahari K
Department of Oral Medicine and Radiology, J.S.S. Dental College and Hospital, S.S. Nagar, Mysore - 15, India.
J Indian Soc Pedod Prev Dent. 2007 Mar;25(1):30-5. doi: 10.4103/0970-4388.31987.
Plexiform neurofibroma is a non-circumscribed, thick and irregular benign tumor of the peripheral nerve sheath. It is a virtually pathognomonic and often disabling feature of neurofibromatosis type I. The diffuse and soft nature of plexiform neurofibroma is often compared to 'a bag of worms' and is difficult to distinguish from a vascular malformation or a lymphangioma, thus necessitating thorough clinical and histopathological examination and imaging of the lesion. We present a case of plexiform neurofibroma in a 12-year-old male child.
丛状神经纤维瘤是一种外周神经鞘的非局限性、粗大且不规则的良性肿瘤。它实际上是I型神经纤维瘤病的特征性表现，且常导致功能障碍。丛状神经纤维瘤质地弥漫且柔软，常被比作“一袋蠕虫”，难以与血管畸形或淋巴管瘤区分开来，因此需要对病变进行全面的临床、组织病理学检查及影像学检查。我们报告一例12岁男性儿童的丛状神经纤维瘤病例。
