Valmaggia C, Helbig H, Fretz C
Augenklinik, Kantonsspital St. Gallen, St. Gallen, Switzerland.
Klin Monbl Augenheilkd. 2007 Apr;224(4):317-9. doi: 10.1055/s-2007-962839.
The idiopathic uveal effusion syndrome is characterized by a spontaneous serous detachment of the choroid and ciliary body. Pathophysiology is related to a relative scleral impermeability to protein. A possible complication is the development of a serous retinal detachment.
We present a 65-year-old male, mild hyperopic patient with a peripheral circular choroidal tumour OD, and macular retinal folds OU. Visual acuity was OD 0.5 due to an additional cataract and OS 1.0. Ocular inflammation was not present. Extensive medical, serological and immunological investigations were normal. On MRI a thicker sclera compatible with the diagnosis was measured.
Twelve months after the first presentation the patient has no complaints and the ocular findings are stable so that a therapy was not necessary up to now.
Uveal effusion syndrome is a rare disease which belongs to the differential diagnosis of choroidal tumour with serous retinal detachment. The correct diagnosis is important as sclerectomy or sclerotomy may be an effective treatment.
特发性葡萄膜渗漏综合征的特征是脉络膜和睫状体自发性浆液性脱离。病理生理学与巩膜对蛋白质的相对不渗透性有关。一种可能的并发症是浆液性视网膜脱离的发生。
我们报告一名65岁男性,轻度远视患者,右眼有周边圆形脉络膜肿瘤,双眼有黄斑视网膜皱褶。右眼因合并白内障视力为0.5,左眼视力为1.0。无眼部炎症。广泛的医学、血清学和免疫学检查均正常。磁共振成像显示测量到与诊断相符的较厚巩膜。
首次就诊12个月后,患者无不适,眼部检查结果稳定,截至目前无需治疗。
葡萄膜渗漏综合征是一种罕见疾病,属于伴有浆液性视网膜脱离的脉络膜肿瘤的鉴别诊断范畴。正确诊断很重要,因为巩膜切除术或巩膜切开术可能是一种有效的治疗方法。