[多哥镰状细胞贫血患儿的阴茎异常勃起]

[Stuttering priapism in children with sickle cell anemia in Togo].

作者信息

Gbadoé A D, Géraldo A, Guédénon K, Koffi S, Agbétiafa K, Akpako P

机构信息

Service de pédiatrie, hôpital CHU-Tokoin, université de Lomé, BP 8881, Lomé, Togo.

出版信息

Arch Pediatr. 2007 Jul;14(7):861-3. doi: 10.1016/j.arcped.2007.03.013. Epub 2007 Apr 24.

DOI:10.1016/j.arcped.2007.03.013

PMID:17459679

Abstract

AIM

To describe clinical aspects and outcome of stuttering priapism (SP) in children with sickle cell anemia.

PATIENTS AND METHODS

We included the 8 children with sickle cell anemia suffering from SP between 1996 and 2004.

RESULTS

Age at onset of SP ranged from 5 to 14 years (mean 9.75+/-3.69 years). SP attacks occurred once a day for 6 patients, and 2 and 3 times by week for the others. It happened during deep sleep, especially in the night (all patients) and sometimes in the day (4 patients). The duration of attacks ranged from 10 min to 2 h in 6 patients and 4 to 5 h in 2 patients. Oral étilefrine was administered to all patients until the cessation of attacks, and continued during 1 month. A long remission was obtained in all patients after 7 days to 7 months treatment (follow-up 2 to 7 years) in spite of 1 or many relapses.

摘要

目的

描述镰状细胞贫血患儿口吃性阴茎异常勃起（SP）的临床特征及转归。

患者与方法

纳入1996年至2004年间8例患有SP的镰状细胞贫血患儿。

结果

SP发病年龄为5至14岁（平均9.75±3.69岁）。6例患者SP发作每天1次，其余患者每周发作2至3次。发作发生在深度睡眠时，尤其是夜间（所有患者），有时也发生在白天（4例患者）。6例患者发作持续时间为10分钟至2小时，2例患者为4至5小时。所有患者均给予口服乙苯福林直至发作停止，并持续1个月。尽管有1次或多次复发，但经过7天至7个月的治疗（随访2至7年）后，所有患者均获得了长期缓解。