Dirschka T, Jackowski J, Bierhoff E, Fölster-Holst R
Dermatologische Praxis Wuppertal, Schuchardstrasse 15, 42275 Wuppertal, Germany.
Hautarzt. 2007 Jul;58(7):611-4. doi: 10.1007/s00105-006-1277-6.
A 15-year-old patient developed scleroderma en coup de sabre on right temple at 5 years of age. Multiple treatments (3 cycles of intravenous penicillin, topical glucocorticosteroids, topical calcipotriol, and cream PUVA phototherapy combined with topical calcipotriol) produced no improvement. The patient suffered greatly from the psychosocial stigmatization, so that the entire lesion was resected at 14 years of age. One year after the operation a thin non-sclerotic scar was present; tiny lateral areas of sclerosis not included in the operative field were unchanged. The operation greatly improved the patient's daily life. The surgical therapy of scleroderma en coup de sabre offers an interesting therapeutic alternative.
一名15岁患者5岁时右颞部出现剑伤样硬皮病。多种治疗方法（3个周期的静脉注射青霉素、外用糖皮质激素、外用卡泊三醇以及补骨脂素紫外线A光疗法联合外用卡泊三醇）均未见改善。患者因心理社会污名化而饱受折磨，因此在14岁时将整个病损切除。术后一年，出现一条薄的非硬化性瘢痕；手术区域未包括的微小硬化侧方区域未改变。手术极大地改善了患者的日常生活。剑伤样硬皮病的手术治疗提供了一种有趣的治疗选择。
