Malhotra Surender, Patel Rakesh N, Mandawat Mahendra
Medical College of Georgia, Evans, GA 30809, USA.
J Invasive Cardiol. 2007 May;19(5):E139-41.
Congenitally corrected transposition of the great vessels (CCTGA) is a rare congenital heart defect. Patients with CCTGA have the anatomical right ventricle as their systemic pumping chamber, with ventricular dysfunction and congestive heart failure (CHF) being relatively common in older adults. The most common presenting feature is bradycardia due to high-degree atrioventricular (AV) blocks. Patients with CCTGA are increasingly subject to CHF with advancing age; this complication is extremely common by the fourth decade. The majority of patients have an inverted coronary arterial pattern.1 We report a case of a patient with CCTGA who presented with rare but life-threatening ventricular tachycardia (VT) leading to syncope, with preserved systemic ventricular function. Coincidentally, the patient also had a single coronary ostium.
先天性矫正型大动脉转位(CCTGA)是一种罕见的先天性心脏缺陷。患有CCTGA的患者以解剖学上的右心室作为其体循环泵血腔,心室功能障碍和充血性心力衰竭(CHF)在老年人中相对常见。最常见的表现特征是由于高度房室(AV)阻滞导致的心动过缓。随着年龄的增长,CCTGA患者越来越容易出现CHF;到第四个十年时,这种并发症极为常见。大多数患者有冠状动脉走行倒置的情况。我们报告一例CCTGA患者,该患者出现罕见但危及生命的室性心动过速(VT)并导致晕厥,而体循环心室功能保留。巧合的是,该患者还只有一个冠状动脉开口。