头皮转移性血管肉瘤导致卡萨巴赫-梅里特综合征。

Metastatic angiosarcoma of the scalp causing Kasabach-Merritt syndrome.

作者信息

Salameh Fares, Henig Israel, Bar-Shalom Rachel, Maza Itay

机构信息

Department of Internal Medicine B, Rambam Medical Center, and B. Rappaport Faculty of Medicine, Technion, Haifa, Israel.

出版信息

Am J Med Sci. 2007 May;333(5):293-5. doi: 10.1097/MAJ.0b013e318053e1e5.

DOI:10.1097/MAJ.0b013e318053e1e5

PMID:17505172

Abstract

We report a case of thrombocytopenia caused by Kasabach-Merritt syndrome (KMS) in a 69-year-old man with a metastatic angiosarcoma of the scalp. A review of the literature revealed that only 4 cases of KMS associated with angiosarcoma have been previously reported. All these cases occurred with a solitary large lesion. This is the first case of thrombocytopenia caused by KMS associated with small metastatic lesions of angiosarcoma that developed after the primary lesion has been completely removed.

摘要

我们报告一例69岁男性头皮转移性血管肉瘤患者发生卡萨巴赫-梅里特综合征（KMS）所致的血小板减少症。文献回顾显示，此前仅报道过4例与血管肉瘤相关的KMS病例。所有这些病例均伴有单个大病灶。这是首例原发性病灶已完全切除后发生的、由KMS所致血小板减少症，且与血管肉瘤小转移病灶相关。