转移性血管肉瘤与卡萨巴赫-梅里特综合征。

Massarweh Suleiman, Munis Aun, Karabakhtsian Rouzan, Romond Edward, Moss Jessica

Department of Internal Medicine, University of Kentucky , Lexington, KY, USA.

Rare Tumors. 2014 Jun 13;6(2):5366. doi: 10.4081/rt.2014.5366. eCollection 2014 May 13.

Angiosarcomas are exceedingly rare tumors that are often difficult to diagnose. Exceptionally unusual is the presentation of these tumors with Kasabach-Merritt Syndrome, a curious form of intratumoral coagulation that can be impossible to distinguish from intravascular coagulation, which is more common. Instant recognition of this clinical association can help making a prompt diagnosis and timely initiation of therapy.

血管肉瘤是极其罕见的肿瘤，通常难以诊断。这些肿瘤伴有卡萨巴赫-梅里特综合征的表现极为罕见，这是一种奇特的肿瘤内凝血形式，可能无法与更常见的血管内凝血区分开来。立即识别这种临床关联有助于迅速做出诊断并及时开始治疗。