Im G J, Jung H H
Department of Otolaryngology-Head and Neck Surgery, College of Medicine, Korea University, Seoul, South Korea.
J Laryngol Otol. 2008 Mar;122(3):310-3. doi: 10.1017/S0022215107008742. Epub 2007 May 25.
Cogan's syndrome is a rare clinical entity that is characterised by non-syphilitic interstitial keratitis and audiovestibular symptoms. The cause of Cogan's syndrome is considered to be autoimmune disease, which is supported by the resolution of hearing loss after steroid treatment, and the association with other autoimmune diseases. The sensorineural hearing loss of Cogan's syndrome is progressive over a few months, and sudden, bilateral deafness often occurs, which may be an indication for cochlear implantation. This paper presents the case of a young woman suffering from Cogan's syndrome and sudden, bilateral deafness. With reference to this case, we describe problems regarding cochlear implantation for Cogan's syndrome and radiological findings aiding selection of cochlear implantation side.
科根综合征是一种罕见的临床病症，其特征为非梅毒性间质性角膜炎和听前庭症状。科根综合征的病因被认为是自身免疫性疾病，这一观点得到了类固醇治疗后听力损失症状缓解以及与其他自身免疫性疾病相关联的支持。科根综合征的感音神经性听力损失在数月内呈进行性发展，且常突然出现双侧耳聋，这可能是人工耳蜗植入的指征。本文介绍了一名患有科根综合征并突然出现双侧耳聋的年轻女性病例。参照该病例，我们描述了科根综合征人工耳蜗植入相关问题以及有助于选择人工耳蜗植入侧的影像学检查结果。
