Cogan 综合征患者行人工耳蜗植入术后的言语感知：遵循 CARE 指南的病例系列研究。
Speech reception after cochlear implantation for Cogan's syndrome: Case series following CARE guidelines.
机构信息
Service ORL et chirurgie cervico-faciale, CHRU de Tours, 2, boulevard Tonnellé, 37044 Tours, France.
Service ORL et chirurgie cervico-faciale, CHU d'Angers, 4, rue Larrey, 49000 Angers, France.
出版信息
Eur Ann Otorhinolaryngol Head Neck Dis. 2023 Sep;140(5):235-238. doi: 10.1016/j.anorl.2023.06.005. Epub 2023 Jul 19.
INTRODUCTION
Cogan's syndrome is a rare form of vasculitis mainly affecting young subjects of whatever gender, associating cochleovestibular and ophthalmological damage. Despite medical treatment, auditory prognosis is uncertain, with 50-60% of patients showing irreversible severe to profound hearing loss, thus being candidates for cochlear implantation. Following CARE guidelines, we report 10 cases of cochlear implantation in Cogan's syndrome, with assessment of speech reception threshold and maximum intelligibility after a minimum 1 year's experience with the implant.
CASE SERIES
Ten patients from 4 centers received cochlear implants (14 implants) for Cogan's syndrome between 2005 and 2020. After 1 year's experience, there was significant improvement in speech reception threshold (P=0.0002) and maximum intelligibility (P=0.0002).
CONCLUSION-DISCUSSION: Audiovestibular signs associated with ophthalmological manifestations should suggest Cogan's syndrome. Hearing impairment is usually irreversible. Cochlear implantation may be necessary and improves hearing performance.
简介
Cogan 综合征是一种罕见的脉管炎形式，主要影响任何性别、年龄的年轻患者，伴有耳蜗-前庭和眼部损害。尽管进行了医学治疗，但是听力预后仍不确定，50-60%的患者出现不可逆的严重至重度听力损失，因此是耳蜗植入的候选者。根据 CARE 指南，我们报告了 10 例 Cogan 综合征的耳蜗植入病例，评估了植入后至少 1 年的言语接受阈和最大可懂度。
病例系列
4 个中心的 10 名患者（14 个植入物）在 2005 年至 2020 年间因 Cogan 综合征接受了耳蜗植入。植入 1 年后，言语接受阈（P=0.0002）和最大可懂度（P=0.0002）有显著改善。
结论讨论
伴有眼部表现的听觉-前庭征象应提示 Cogan 综合征。听力损害通常是不可逆的。耳蜗植入可能是必要的，并且可以改善听力表现。
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