Tropomyosin in the groove? Molecular insights into an inherited myopathy.
作者信息
Chase P Bryant
机构信息
Florida State University, Department of Biological Science, Tallahassee, FL, USA.
出版信息
J Physiol. 2007 Jun 15;581(Pt 3):889. doi: 10.1113/jphysiol.2007.135517. Epub 2007 May 24.
Abstract
摘要
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Effects of a R133W beta-tropomyosin mutation on regulation of muscle contraction in single human muscle fibres.R133Wβ-原肌球蛋白突变对单根人肌纤维肌肉收缩调节的影响。
J Physiol. 2007 Jun 15;581(Pt 3):1283-92. doi: 10.1113/jphysiol.2007.129759. Epub 2007 Apr 12.
2
Distal arthrogryposis and muscle weakness associated with a beta-tropomyosin mutation.与β-原肌球蛋白突变相关的远端关节挛缩症和肌肉无力。
Neurology. 2007 Mar 6;68(10):772-5. doi: 10.1212/01.wnl.0000256339.40667.fb.
3
Thin-filament regulation of force redevelopment kinetics in rabbit skeletal muscle fibres.兔骨骼肌纤维中细肌丝对力量重建动力学的调节
J Physiol. 2007 Mar 1;579(Pt 2):313-26. doi: 10.1113/jphysiol.2006.124164. Epub 2007 Jan 4.
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Mutations in fast skeletal troponin I, troponin T, and beta-tropomyosin that cause distal arthrogryposis all increase contractile function.导致远端关节挛缩症的快速骨骼肌肌钙蛋白I、肌钙蛋白T和β-原肌球蛋白的突变均会增强收缩功能。
FASEB J. 2007 Mar;21(3):896-905. doi: 10.1096/fj.06-6899com. Epub 2006 Dec 27.
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Ca2+ sensitivity of regulated cardiac thin filament sliding does not depend on myosin isoform.受调控的心脏细肌丝滑动的钙离子敏感性不依赖于肌球蛋白同工型。
J Physiol. 2006 Dec 15;577(Pt 3):935-44. doi: 10.1113/jphysiol.2006.120105. Epub 2006 Sep 28.
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Molecular and cellular aspects of troponin cardiomyopathies.肌钙蛋白心肌病的分子与细胞层面
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