Takeuchi Ichiro, Kawaguchi Takeo, Kimura Yuichiro, Kojima Jisho, Shimamura Hiromasa, Shimizu Noritaka, Izumi Tohru
Department of Cardiology, Odawara Municipal Hospital, Odawara, Japan.
Intern Med. 2007;46(10):649-51. doi: 10.2169/internalmedicine.46.6267. Epub 2007 May 24.
A primary cardiac malignant tumor is very rare; its prevalence is only 0.002-0.28%. Among most malignant tumors, angiosarcoma, leiomyosarcoma, and mesothelioma occupy the majority. A cardiac osteosarcoma is extremely rare: to our knowledge, only 36 cases have been reported worldwide. We present a 22-year-old case featuring severe congestive heart failure. Hemodynamically the tumor led to significant obstruction of the mitral valve. The patient underwent an emergency resection operation, but multiple metastases occurred. Though the characteristics still remain unclear because of the low prevalence, it is very important that these tumors be distinguished from benign tumors because of early resection operation.
原发性心脏恶性肿瘤非常罕见，其发病率仅为0.002% - 0.28%。在大多数恶性肿瘤中，血管肉瘤、平滑肌肉瘤和间皮瘤占多数。心脏骨肉瘤极其罕见：据我们所知，全球仅报道过36例。我们报告一例22岁的病例，其表现为严重的充血性心力衰竭。从血流动力学角度看，肿瘤导致二尖瓣严重梗阻。患者接受了急诊切除手术，但发生了多处转移。尽管由于发病率低，其特征仍不明确，但由于需要早期进行切除手术，因此将这些肿瘤与良性肿瘤区分开来非常重要。
