Kobayashi O
Department of Medicine (II), Niigata University School of Medicine.
Nihon Kyobu Shikkan Gakkai Zasshi. 1991 Aug;29(8):1007-16.
The ultrastructure of pulmonary alveolar capillaries in idiopathic interstitial pneumonia (IIP) and collagen vascular diseases (CVD) were investigated. In IIP, the endothelial cells were only slightly swollen. The basement membrane (BM) was moderately thickened. In CVD, swelling of the endothelial cells and thickening of the BM were more severe than those of IIP. The injury of the endothelial cells seemed to be more severe than IIP. The patients with PSS and MCTD revealed degeneration of endothelial cells as well as lamellation of BM. The endothelial cell damage was most severe among CVD cases, and these changes were assumed to induce pulmonary hypertension. Microtubular structures were observed in the endothelium of SLE, dermatomyositis, polymyositis, PSS and MCTD patients. Weibel-Palade bodies and increase of pericytes were noticed in PSS and MCTD patients which seemed to be related to endothelial injuries. No electron-dense deposits were observed in any case.
对特发性间质性肺炎(IIP)和胶原血管疾病(CVD)中肺泡毛细血管的超微结构进行了研究。在IIP中,内皮细胞仅轻微肿胀。基底膜(BM)中度增厚。在CVD中,内皮细胞肿胀和BM增厚比IIP更严重。内皮细胞的损伤似乎比IIP更严重。患有系统性硬化症(PSS)和混合性结缔组织病(MCTD)的患者表现出内皮细胞变性以及BM分层。在CVD病例中,内皮细胞损伤最为严重,并且这些变化被认为会诱发肺动脉高压。在系统性红斑狼疮(SLE)、皮肌炎、多发性肌炎、PSS和MCTD患者的内皮中观察到微管结构。在PSS和MCTD患者中注意到了魏-帕小体(Weibel-Palade bodies)和周细胞增多,这似乎与内皮损伤有关。在任何病例中均未观察到电子致密沉积物。