Sherman J H, Le B H, Okonkwo D O, Jane J A
Department of Neurological Surgery, University of Virginia, Charlottesville, Virginia, USA.
Acta Neurochir (Wien). 2007;149(9):969-72; discussion 972. doi: 10.1007/s00701-007-1180-7. Epub 2007 Jun 11.
Hemangioblastomas are rarely found in a supratentorial location and are commonly associated with the von Hippel-Lindau complex. Therefore, patients with such tumors must be evaluated for both other hemangioblastomas within the central nervous system as well as for this complex via physical examination, radiographic examination, and genetic testing. We report the seventh case of a patient with an isolated supratentorial dural based hemangioblastoma not associated with the von Hippel-Lindau complex.
血管母细胞瘤很少出现在幕上部位,通常与冯·希佩尔-林道综合征相关。因此,对于患有此类肿瘤的患者,必须通过体格检查、影像学检查和基因检测,对中枢神经系统内的其他血管母细胞瘤以及该综合征进行评估。我们报告了第七例孤立的幕上硬脑膜血管母细胞瘤患者,该肿瘤与冯·希佩尔-林道综合征无关。