Nagasaka Toru, Hayashi Shigemasa, Naito Takehiro, Okamoto Takeshi, Ikeda Hiroshi, Inao Suguru
Department of Neurosurgery, Japanese Red Cross Nagoya First Hospital, Nagoya, Japan.
J Neurosurg. 2007 May;106(5 Suppl):388-90. doi: 10.3171/ped.2007.106.5.388.
Moyamoya disease is categorized as either ischemic or hemorrhagic type, and the pathogenesis of this disease is unknown. In this paper, the authors report on a patient with moyamoya disease who suffered concomitant cerebral infarction and intraventricular hemorrhage (IVH). Endoscopic removal of the intraventricular hematoma and ventricular drainage were both performed. The patient did not experience further ischemic complications. Patients with moyamoya disease have intracranial hemodynamic insufficiency. Adequate control of intracranial pressure and removal of the intraventricular hematoma is important to prevent progression of cerebral infarction and hydrocephalus. To the authors' knowledge, this is the first report of concomitant cerebral infarction and IVH, or true mixed-type moyamoya disease. A possible pathogenesis of this rare condition is discussed.
烟雾病分为缺血型或出血型，其发病机制尚不清楚。在本文中，作者报告了一名患有烟雾病并伴有脑梗死和脑室内出血（IVH）的患者。进行了脑室内血肿的内镜清除和脑室引流。该患者未出现进一步的缺血性并发症。烟雾病患者存在颅内血流动力学不足。充分控制颅内压和清除脑室内血肿对于预防脑梗死进展和脑积水很重要。据作者所知，这是关于同时存在脑梗死和IVH，即真正的混合型烟雾病的首例报告。本文讨论了这种罕见情况的可能发病机制。
