Josan Vivek, Smith Paul, Kornberg Andrew, Rickert Christian, Maixner Wirginia
Department of Neurosurgery, Royal Children's Hospital, Melbourne, Victoria, Australia.
J Neurosurg. 2007 Jun;106(6 Suppl):509-12. doi: 10.3171/ped.2007.106.6.509.
Dysembryoplastic neuroepithelial tumors (DNETs) are benign supratentorial tumors based in the cerebral cortex. They usually are found in children and young adults with seizures that tend to become refractory to medical treatment. In the vast majority of cases resection results in good seizure control, and adjuvant therapy is not required. When tumors thought to be DNETs are not resected due to their proximity to eloquent cortex, lack of change in the clinical and neuroimaging features over time supports the diagnosis of DNET. The authors report on a patient in whom a pilocytic astrocytoma developed within a DNET, raising questions regarding the classification of these lesions and the need for lifelong clinical and imaging surveillance. This paper adds to the growing body of literature about the biological behavior of these lesions.
胚胎发育不良性神经上皮肿瘤(DNETs)是位于大脑皮质的良性幕上肿瘤。它们通常在患有癫痫发作的儿童和年轻人中发现,这些癫痫发作往往对药物治疗变得难治。在绝大多数情况下,切除可实现良好的癫痫控制,且不需要辅助治疗。当被认为是DNETs的肿瘤由于靠近功能区皮质而未被切除时,随着时间推移临床和神经影像学特征无变化支持DNET的诊断。作者报告了1例在DNET内发生毛细胞型星形细胞瘤的患者,这引发了关于这些病变分类以及终身临床和影像学监测必要性的问题。本文增加了关于这些病变生物学行为的不断增长的文献。