Engvall Monica, Sjögreen Lotta, Kjellberg Heidrun, Robertson Agneta, Sundell Sten, Kiliaridis Stavros
Department of Pedodontics, Institute of Odontology, Göteborg University, Sweden.
Eur J Oral Sci. 2007 Jun;115(3):192-7. doi: 10.1111/j.1600-0722.2007.00446.x.
Myotonic dystrophy or dystrophia myotonica (DM) is a hereditary neuromuscular multisystem disease with a varying clinical expressivity and severity. The objective of this study was to assess the oral health in children with myotonic dystrophy and to compare it with a control group. Fifty-six DM patients, aged 2.7-18.0 yr, were compared with age- and gender-matched control patients with respect to caries, plaque, and gingivitis. Oral function and signs of temporomandibular dysfunction (TMD) were assessed, and the ability to co-operate in dental treatment was estimated. Questionnaires concerning eating habits, dental care, traumatic injuries to teeth, and orofacial function were also used. The DM patients had significantly more caries, plaque, and gingivitis than did control patients. They had more TMD problems and lower co-operation ability than the healthy control persons. General sedation was frequently needed to carry through dental treatment. DM patients are at risk of caries, gingivitis and TMD problems, and need intensified prophylactic care. Behavior management problems are common.
强直性肌营养不良症或萎缩性肌强直（DM）是一种遗传性神经肌肉多系统疾病，临床表型和严重程度各异。本研究的目的是评估强直性肌营养不良症患儿的口腔健康状况，并与对照组进行比较。将56例年龄在2.7至18.0岁之间的DM患者与年龄和性别匹配的对照患者在龋齿、牙菌斑和牙龈炎方面进行比较。评估口腔功能和颞下颌关节紊乱（TMD）体征，并评估其在牙科治疗中的合作能力。还使用了关于饮食习惯、口腔护理、牙齿外伤和口面部功能的问卷。DM患者的龋齿、牙菌斑和牙龈炎明显多于对照患者。他们比健康对照者有更多的TMD问题，合作能力更低。牙科治疗通常需要全身镇静。DM患者有患龋齿、牙龈炎和TMD问题的风险，需要加强预防性护理。行为管理问题很常见。
