Sarmiento de la Iglesia M M, Peña B, Lecumberri G, Oleaga L, Grande Icaran D
Servicio de Radiodiagnóstico, Hospital de Basurto, Bilbao, Spain.
Radiologia. 2007 Jul-Aug;49(4):269-71. doi: 10.1016/s0033-8338(07)73769-4.
Multicystic dysplasia of the kidney is the second most common cause of renal masses in newborns after hydronephrosis and the most frequent cause of cystic masses in childhood. We present the case of a cystic renal mass in an infant that was definitively diagnosed at histological examination to be segmental cystic dysplasia. Cystic renal dysplasia usually involves an entire kidney, and segmental multicystic renal dysplasia is rare. We review the etiology and pathogenesis of this entity, the radiological findings, and the main differential diagnoses with the aim of establishing the correct diagnosis and differentiating this entity from other focal cystic kidney lesions affecting children.
多囊性肾发育不良是新生儿肾肿块继肾积水之后的第二大常见病因，也是儿童期囊性肿块的最常见病因。我们报告一例婴儿囊性肾肿块病例，经组织学检查确诊为节段性囊性发育不良。囊性肾发育不良通常累及整个肾脏，节段性多囊性肾发育不良较为罕见。我们回顾该疾病的病因、发病机制、影像学表现及主要鉴别诊断，旨在确立正确诊断，并将该疾病与影响儿童的其他局灶性囊性肾病变相鉴别。
