Kajbafzadeh Abdolmohammad
Department of Pediatric Urology, Children's Hospital Medical Center, Tehran University of Medical Sciences, Tehran, Iran.
Urol J. 2005 Summer;2(3):125-31.
In the second part of this article, congenital urethral anomalies other than posterior urethral valve were reviewed.
The anomalies considered in the current review were anterior urethral valve, lacuna magna, syringocele, Cobb's collar, duplication of urethra, megalourethra, and prostatic urethral polyps. The literature was extensively reviewed concerning the presentations, diagnosis, different types of treatment modalities, morbidity, mortality, and new concepts for the above disorders.
Anterior urethral valves or diverticula are the most prevalent congenital anomalies of anterior urethra. The lacuna magna is the largest depression in the dorsal aspect of the fossa navicularis. It is demonstrable on a well-performed voiding cystourethrography of the distal urethra. The dilated Cowper's gland duct is the other missed diagnosed anomaly of the urethra in boys. The congenital narrowing of the bulbar urethra with a variable clinical presentation and obstruction grade and different types of anterior urethral obstruction are the most common presentation of these anomalies. However, other symptoms or signs including, hematuria, bloody spotting on underwear, discomfort or sever pain in the vicinity of the glance, interrupted voiding, infection, bulging of anterior urethra, enuresis, and postvoiding dribbling are the only nonspecific manifestations of these disorders.
All of these disorders are demonstrable on a well-performed voiding cystourethrography of the distal urethra. The urologist must be aware about these uncommon congenital anomalies and the anterior urethra should be carefully evaluated for such anomalies. Diagnosis of these entities is elusive unless the physician is looking for them. Nonspecific symptoms mentioned here besides radiographic findings can be a valuable clue for diagnosis.
在本文的第二部分,对除后尿道瓣膜之外的先天性尿道异常进行了综述。
本次综述所考虑的异常包括前尿道瓣膜、舟状窝巨窝、尿道囊肿、科布氏束带、尿道重复、巨尿道和前列腺尿道息肉。广泛查阅了有关上述疾病的临床表现、诊断、不同类型的治疗方式、发病率、死亡率及新概念的文献。
前尿道瓣膜或憩室是前尿道最常见的先天性异常。舟状窝巨窝是舟状窝背侧最大的凹陷,在良好的远端尿道排尿性膀胱尿道造影中可显示。扩张的尿道球腺导管是男孩中另一种易漏诊的尿道异常。球部尿道先天性狭窄,临床表现、梗阻程度各异,以及不同类型的前尿道梗阻是这些异常最常见的表现。然而,血尿、内裤上的血性斑点、阴茎附近的不适或剧痛、排尿中断、感染、前尿道膨出、遗尿和排尿后滴沥等其他症状或体征是这些疾病仅有的非特异性表现。
所有这些疾病在良好的远端尿道排尿性膀胱尿道造影中均可显示。泌尿外科医生必须了解这些不常见的先天性异常,并且应仔细评估前尿道是否存在此类异常。除非医生刻意寻找,否则这些疾病的诊断难以捉摸。除影像学表现外,这里提到的非特异性症状可能是诊断的重要线索。