Mekni A, Maamouri N, Zidi Y, Braham E, Fareh F, Bellil K, Haouet S, Kchir N, Jilani S B, Zitouna M
Department of Pathology, Hospital "La Rabta", Bab Saadoun, Tunis, Tunisie.; ' Department of Gastroenterology,
Pathologica. 2007 Apr;99(2):54-6.
Desmoplastic small round cell tumor (DSRCT) is a rare clinicopathological entity individualized in 1989. Its etiopathogenesis is still unknown, and diagnosis can be achieved only by immunohistochemistry and cytogenetic studies. The objective of this work is to report two new cases of DSRCT and to review the literature to clarify its epidemiological, clinical and pathological aspects.
促结缔组织增生性小圆细胞肿瘤（DSRCT）是1989年确定的一种罕见的临床病理实体。其病因仍不明，仅通过免疫组织化学和细胞遗传学研究才能确诊。本文旨在报告两例DSRCT新病例并复习文献以阐明其流行病学、临床和病理特征。
