Kletter Gad B, Sweetser David A, Wallace Steven F, Sawin Robert S, Rutledge Joe C, Geyer J Russell
Pediatric Endocrine, Swedish Physician Division 1101 Madison, Suite # 800, Seattle, WA 98104, USA.
J Pediatr Endocrinol Metab. 2007 May;20(5):639-42. doi: 10.1515/jpem.2007.20.5.639.
We present a 3-year-old child with Cushing's syndrome due to an ACTH-secreting metastatic pancreatoblastoma. This malignancy is a rare cause of Cushing's syndrome, particularly at pediatric age. We describe her course including the use of ketoconazole to alleviate hypercortisolemia.
我们报告一名3岁儿童因分泌促肾上腺皮质激素(ACTH)的转移性胰腺母细胞瘤而患有库欣综合征。这种恶性肿瘤是库欣综合征的罕见病因,尤其是在儿童期。我们描述了她的病程,包括使用酮康唑来缓解高皮质醇血症。