Moon H, Lee Y J, Lee S I, Yoo W H
Division of Rheumatology, Department of Internal Medicine, Chonbuk National University Medical School, Institute of Clinical Medicine, #634-18, Geum-Am Dong, Duck-Jin Gu, Jeonju, Chonbuk, 561-712, South Korea.
Rheumatol Int. 2008 Feb;28(4):375-7. doi: 10.1007/s00296-007-0426-2. Epub 2007 Aug 3.
Behcet's disease (BD) is a chronic relapsing systemic vasculitic disorder affecting the arteries, veins, and vessels of any size. Large vein thrombosis in BD is not commonly developed and most commonly observed in the veins in the lower extremities and inferior or superior vena cava. In this report, a 18-year-old male patient with large vein thrombosis involving superior vena cava was presented. He was treated due to chylothorax and chylopericardium with SVC syndrome before diagnosis of BD. SVC thrombosis complicated by chylothorax and chyolpericardium can be a rare presenting initial symptom of BD.
白塞病（BD）是一种慢性复发性全身性血管炎疾病，可累及动脉、静脉及任何大小的血管。白塞病中发生大静脉血栓形成并不常见，最常发生于下肢静脉以及下腔静脉或上腔静脉。在本报告中，我们介绍了一名18岁男性患者，其发生了累及上腔静脉的大静脉血栓形成。在诊断白塞病之前，他因乳糜胸和乳糜心包伴上腔静脉综合征接受了治疗。上腔静脉血栓形成合并乳糜胸和乳糜心包可能是白塞病一种罕见的首发症状。
