Leu-Semenescu Smaranda, Roze Emmanuel, Vidailhet Marie, Legrand André-Pierre, Trocello Jean-Marc, Cochen Valérie, Sangla Sophie, Apartis Emmanuelle
Department of Neurology, Saint-Antoine Hospital, AP-HP, Paris, France.
Mov Disord. 2007 Oct 31;22(14):2063-9. doi: 10.1002/mds.21651.
Patients with Parkinson's disease (PD) often complain of unsteadiness. This can occur as the result of various neurological dysfunctions, including changes in postural adjustments, loss of postural reflexes, axial akinesia and rigidity, freezing and/or postural hypotension. In some cases these symptoms remain unexplained, and rare cases of unsteadiness have been attributed to tremor on standing. To delineate this condition, we investigated 11 consecutive PD patients with unexplained unsteadiness because of tremor on standing, seen in our department over a 6-year period. All the patients had detailed clinical and electrophysiological investigations based on surface polygraphic electromyographic recordings. Four patients had fast orthostatic tremor (13-18 Hz), one had intermediate orthostatic tremor (8-9 Hz), and three had slow orthostatic tremor (4-6 Hz). The remaining 3 patients had orthostatic myoclonus, a condition that has not previously been reported in PD. Patients with fast tremor improved on clonazepam. Patients with slow tremor and myoclonus improved on levodopa and sometimes benefited further when clonazepam was added. These observations show the usefulness of neurophysiological investigations for diagnosing and treating unexplained unsteadiness in Parkinson's disease.
帕金森病(PD)患者常诉说身体不稳。这可能是多种神经功能障碍导致的结果,包括姿势调整改变、姿势反射丧失、轴性运动不能和强直、冻结现象和/或体位性低血压。在某些情况下,这些症状仍无法解释,少数身体不稳的病例被归因于站立时的震颤。为了明确这种情况,我们对连续11例因站立时震颤导致身体不稳且原因不明的PD患者进行了调查,这些患者是在我们科室6年期间接诊的。所有患者都基于表面多导肌电图记录进行了详细的临床和电生理检查。4例患者有快速直立性震颤(13 - 18赫兹),1例有中度直立性震颤(8 - 9赫兹),3例有慢速直立性震颤(4 - 6赫兹)。其余3例患者有直立性肌阵挛,这是一种此前在PD中未被报道过的情况。快速震颤患者使用氯硝西泮后病情改善。慢速震颤和肌阵挛患者使用左旋多巴后病情改善,有时加用氯硝西泮后进一步获益。这些观察结果表明神经生理检查对于诊断和治疗帕金森病中原因不明的身体不稳是有用的。