Erro Roberto, Bhatia Kailash P, Cordivari Carla
Sobell Department of Motor Neuroscience and Movement Disorders UCL Institute of Neurology London United Kingdom.
Dipartimento di Scienze Neurologiche e del Movimento Università di Verona Verona Italy.
Mov Disord Clin Pract. 2014 Jun 12;1(3):173-179. doi: 10.1002/mdc3.12053. eCollection 2014 Sep.
Orthostatic tremor is a rare condition, though its exact prevalence is unknown, which is clinically characterized by a feeling of unsteadiness or being about to fall on standing and which disappears on walking, sitting, or lying down. It is generally accepted that classic orthostatic tremor manifests with a high-frequency tremor (>13 Hz) of the legs when standing. However, a number of patients initially reported as orthostatic tremor did not actually have such electrophysiological features. It is our experience that there is a clinical spectrum of different conditions presenting as shaking on standing, and this highlights the importance of the electrophysiology to aid the differential diagnosis of these disorders. Here, we provide a critical review of the clinical spectrum of shaking on standing, along with demonstrative electrophysiological recordings of some of these conditions.
直立性震颤是一种罕见病症，尽管其确切患病率尚不清楚，其临床特征为站立时感到不稳或即将跌倒，而在行走、坐下或躺下时消失。人们普遍认为，典型的直立性震颤在站立时表现为腿部高频震颤（>13赫兹）。然而，一些最初被报告为直立性震颤的患者实际上并没有这种电生理特征。我们的经验是，存在一系列不同病症的临床谱，这些病症表现为站立时颤抖，这凸显了电生理检查在辅助这些疾病鉴别诊断中的重要性。在此，我们对站立时颤抖的临床谱进行批判性综述，并展示其中一些病症的电生理记录。
