Marchesi D, Rüdeberg A, Aebi M
Clinique Universitaire de Chirurgie Orthopédique, Inselspital, Berne, Suisse.
Acta Orthop Belg. 1991;57(4):390-8.
The advances in urological and neurosurgical management in myelomeningocoele patients have led to an increased survival rate. The extremely complex spinal deformity presents a major treatment challenge. Clinical and radiological evolution of scoliosis treated conservatively for at least 10 years was studied. Eighty-nine myelomeningocoele patients born between 1964 and 1977 were reviewed. Thirty-one (35%) were noted to have scoliosis (10 congenital type, 21 developmental type). All congenital forms showed rapid progression despite brace treatment, often to curvatures in excess of 100 degrees. Among the developmental type, curves detected prior to 10 years (10 cases before 5 years, 6 cases between 6 and 10 years) were rapidly progressive beyond 70 degrees. Curves detected after 10 years (5 patients) never exceeded 30 degrees. Because of this natural history, conservative treatment should be limited to developmental forms less than 50 degrees. Spinal stabilization is indicated in all curvatures over 50 degrees without awaiting adulthood.
脊髓脊膜膨出患者泌尿外科和神经外科治疗方法的进步提高了生存率。极其复杂的脊柱畸形带来了重大的治疗挑战。对保守治疗至少10年的脊柱侧弯患者的临床和影像学演变进行了研究。回顾了1964年至1977年间出生的89例脊髓脊膜膨出患者。其中31例(35%)被发现患有脊柱侧弯(10例先天性,21例发育性)。所有先天性脊柱侧弯尽管采用了支具治疗仍进展迅速,常发展为超过100度的弯曲。在发育性脊柱侧弯类型中,10岁之前检测到的弯曲(5岁之前10例,6至10岁6例)迅速进展超过70度。10岁之后检测到的弯曲(5例患者)从未超过30度。鉴于这种自然病程,保守治疗应仅限于小于50度的发育性脊柱侧弯。所有超过50度的弯曲均应进行脊柱稳定手术,无需等到成年。