Oztekin N S, Saygi S S, Oztekin F, Selekler K
Hacettepe University, School of Medicine, Ankara, Turkey.
J Neurosurg Sci. 1991 Jul-Sep;35(3):153-6.
The temporal lobe agenesis syndrome is a rare congenital abnormality. This syndrome frequently has been described in association with arachnoid cysts or abnormal collections of cerebrospinal fluid. Arachnoid cysts develop most frequently in the middle cranial fossa and almost all these cysts are unilateral. Bilateral middle cranial fossa arachnoid cysts are extremely rare and only 9 cases have been reported in the literature. We present an adult case with bilateral arachnoid cysts and temporal lobe agenesis whose mental examination and neurologic assessment is normal. The cysts are demonstrated by CT and metrizamid CT cysternography.
颞叶发育不全综合征是一种罕见的先天性异常。该综合征常与蛛网膜囊肿或脑脊液异常聚集有关。蛛网膜囊肿最常发生于中颅窝,几乎所有这些囊肿都是单侧的。双侧中颅窝蛛网膜囊肿极为罕见,文献中仅报道过9例。我们报告一例患有双侧蛛网膜囊肿和颞叶发育不全的成年病例,其精神检查和神经学评估均正常。囊肿通过CT和甲泛葡胺CT脑池造影得以显示。