Curfs L M, Wiegers A M, Sommers J R, Borghgraef M, Fryns J P
Observation Center de Hondsberg, Oisterwijk, The Netherlands.
Clin Genet. 1991 Dec;40(6):430-4. doi: 10.1111/j.1399-0004.1991.tb03114.x.
In this report we present the results of a study of the intellectual functioning and cognitive profile of 26 Prader-Willi syndrome (PWS) patients. The mean IQ score was 62.3 (range 39-96). In 13 patients a significant difference between verbal and performance IQ was found. In 10 of them the performance IQ was higher than the verbal. The results of subtest analysis indicate that cognitive strengths are more visible than cognitive weaknesses. Highest scores were noted especially in the performance scale, i.e. Block Design (9 children) and Coding or Mazes (5 children). Analysis of all available data indicates that PWS patients score better on visual motor discrimination skills than on auditory verbal processing skills. These results are promising for intervention programs and education strategies.
在本报告中，我们展示了一项针对26名普拉德-威利综合征（PWS）患者智力功能和认知概况的研究结果。平均智商得分是62.3（范围为39 - 96）。在13名患者中，发现言语智商和操作智商存在显著差异。其中10名患者的操作智商高于言语智商。子测验分析结果表明，认知优势比认知劣势更为明显。尤其在操作量表中得分最高，即积木图案（9名儿童）和译码或迷宫（5名儿童）。对所有可用数据的分析表明，PWS患者在视觉运动辨别技能方面的得分高于听觉言语处理技能。这些结果对干预计划和教育策略很有意义。
