Baillieux Hanne, Weyns Frank, Paquier Philippe, De Deyn Peter P, Mariën Peter
Faculty of Linguistics, Vrije Universiteit Brussel, Brussels, Belgium.
Pediatr Neurosurg. 2007;43(5):386-95. doi: 10.1159/000106388.
The posterior fossa syndrome (PFS) is a well-known clinical consequence of posterior fossa surgery that has only been reported in a limited number of cases with a nontumoral etiology. It consists of transient cerebellar mutism, behavioral abnormalities and personality changes. We describe a 12-year-old child who developed transient cerebellar mutism associated with behavioral and emotional symptoms following rupture of a vermis arteriovenous malformation (AVM). Following the stroke, the girl experienced a 24-hour symptom-free interval. After that, she became mute and her emotional state was characterized by severe anxiety, irritability and withdrawal. After 3 days, mutism resolved and dysarthria became apparent. Two weeks after stroke, the AVM was surgically removed and the postoperative course was uneventful. This case is the first reported in which the PFS occurred after focal nonsurgically induced cerebellar damage.
后颅窝综合征（PFS）是后颅窝手术的一种众所周知的临床后果，仅在少数非肿瘤病因的病例中有所报道。它包括短暂性小脑缄默症、行为异常和性格改变。我们描述了一名12岁儿童，其在小脑蚓部动静脉畸形（AVM）破裂后出现了与行为和情绪症状相关的短暂性小脑缄默症。中风后，该女孩经历了24小时的无症状期。此后，她变得缄默，情绪状态表现为严重焦虑、易怒和退缩。3天后，缄默症消失，构音障碍变得明显。中风两周后，AVM被手术切除，术后过程顺利。该病例是首次报道的在局灶性非手术诱导的小脑损伤后发生PFS的病例。
