Guzelmeric Kadir, Ergen Bahar, Pirimoglu Zehra Meltem, Gecer Melin Ozgun, Unal Orhan, Turan Cem
Department of Obstetrics and Gynecology, Dr. Lutfi Kirdar Kartal Education and Research Hospital, Istanbul, Turkey.
Arch Gynecol Obstet. 2008 Feb;277(2):179-82. doi: 10.1007/s00404-007-0450-1. Epub 2007 Sep 7.
Endometrial stromal sarcoma (ESS) is an uncommon malign neoplasm, and its occurrence outside the uterus is extremely rare in the absence of metastasis or extension of a primary uterine neoplasm. When arising in the pelvis or abdominal cavity, ESS is associated with uterine adnexa or serosal surface of various organs.
We present the case of a 46-year-old woman with lower abdominal pain and regular menstruation who underwent laparotomy after a diagnosis of pelvic mass mimicking a right adnexial tumor. Exploration of the pelvis revealed a retroperitoneal mass of 15 cm in diameter in the right illiac fossa without accompanying pelvic or paraaortic lymphadenopathy. Uterus and ovaries were bilaterally normal in size. The pathology showed low-grade ESS of the uterus with direct spread to retroperitoneum without serosal metastases.
This case shows that despite its well-known good prognostic nature, low-grade ESS may behave as an aggressive malignancy.
子宫内膜间质肉瘤（ESS）是一种罕见的恶性肿瘤，在无原发性子宫肿瘤转移或扩散的情况下，其发生于子宫外的情况极为罕见。当ESS发生于盆腔或腹腔时，与子宫附件或各器官的浆膜面相关。
我们报告一例46岁女性，有下腹痛且月经规律，在诊断为疑似右侧附件肿瘤的盆腔肿块后接受了剖腹手术。盆腔探查发现右髂窝有一个直径15cm的腹膜后肿块，无盆腔或腹主动脉旁淋巴结肿大。子宫和双侧卵巢大小正常。病理显示为低级别子宫ESS，直接蔓延至腹膜后，无浆膜转移。
该病例表明，尽管低级别ESS通常预后良好，但仍可能表现为侵袭性恶性肿瘤。
