Chen Feng, Zhang Chunqing, Wang Wen, Li Lizhen, Yan Shuxin, Sun Jianzhi, Zhang Maohong, Ji Chunyan, Hou Ming
Department of Hematology, Qilu Hospital,Shandong University, Jinan, PR China.
Leuk Res. 2008 Apr;32(4):665-7. doi: 10.1016/j.leukres.2007.08.001. Epub 2007 Sep 12.
Philadelphia-chromosome positive thrombocythemia without features of chronic myeloid leukemia in peripheral blood has been described before. However, there are few reports on Philadelphia-chromosome positive chronic idiopathic myelofibrosis. We present a case of Philadelphia positive chronic idiopathic myelofibrosis that had no obvious response to imatinib.
此前已有关于外周血无慢性髓系白血病特征的费城染色体阳性血小板增多症的描述。然而,关于费城染色体阳性慢性特发性骨髓纤维化的报道较少。我们报告一例对伊马替尼无明显反应的费城染色体阳性慢性特发性骨髓纤维化病例。