肝脏血管周上皮样细胞肿瘤：两例报告并文献复习
Perivascular epithelioid cell tumor of the liver: a report of two cases and review of the literature.
作者信息
Fang Song-Hua, Zhou Li-Na, Jin Mei, Hu Ji-Bo
机构信息
Department of Radiology, Sir Run Run Shaw Hospital, Zhejiang University, Hangzhou 310016, Zhejiang Province , China.
出版信息
World J Gastroenterol. 2007 Nov 7;13(41):5537-9. doi: 10.3748/wjg.v13.i41.5537.
Abstract
Perivascular epithelioid cell tumor (PEComa) is a rare tumor which arises from mesenchymal tissues. It is predominant in the uterus, but very rare in the liver. To the best of our knowledge, less than 5 cases of PEComa of the liver have been reported. Herein we present two pathologically proven cases of PEComa of the liver, retrospectively analyze their clinical and imaging features, and review the literature.
摘要
血管周上皮样细胞瘤（PEComa）是一种起源于间叶组织的罕见肿瘤。它在子宫中较为常见，但在肝脏中非常罕见。据我们所知，肝脏PEComa的报道病例少于5例。在此，我们报告2例经病理证实的肝脏PEComa病例，回顾性分析其临床和影像学特征，并复习相关文献。
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