Department of Nephrology, West China Hospital, Sichuan University, Chengdu, Sichuan Province, China.
Eur Rev Med Pharmacol Sci. 2013 Jun;17(12):1665-8.
Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors containing variable component of smooth muscles, fat and vessels. They occured pretty rare in the liver and no characteristic of imaging data have been demonstrated up to now. We herein present a case of a 58-year-old man with a hepatic PEComa which was correct diagnosed through immunohistochemical confirmation with HMB-45. The clinicopathological and imaging features of hepatic PEComa were analyzed retrospectively. This is the first paper which demonstrated the characteristic of imaging data among liver PEComas and other liver lesions. However, the diagnostic criteria of PEComa depends on pathology. Hepatectomy is the effective treatment.
血管周上皮样细胞瘤(PEComa)是一种间叶性肿瘤,包含平滑肌、脂肪和血管等不同成分。它们在肝脏中较为罕见,目前尚未显示出特征性的影像学数据。本文报告了 1 例 58 岁男性肝脏 PEComa 患者,通过免疫组化 HMB-45 染色明确诊断。回顾性分析肝脏 PEComa 的临床病理和影像学特征。这是首例报告肝脏 PEComa 及其他肝脏病变的影像学特征的文献。然而,PEComa 的诊断标准依赖于病理学。肝切除术是有效的治疗方法。