Zhang Yan-xing, Liu Jian-ren, Jiang Biao, Liu Hui-qin, Ding Mei-ping, Song Shui-jiang, Zhang Bao-rong, Zhang Hong, Xu Bin, Chen Huai-hong, Wang Zhong-jin, Huang Jian-zheng
Department of Neurology, Second Affiliated Hospital, School of Medicine, Zhejiang University, Hangzhou 310009, China.
J Zhejiang Univ Sci B. 2007 Oct;8(10):715-20. doi: 10.1631/jzus.2007.B0715.
Chronic post-hypoxic myoclonus, also known as Lance-Adams syndrome (LAS), is a rare complication of successful cardiopulmanry resuscitation often accompanied by action myoclonus and cerebellar ataxia. It is seen in patients who have undergone a cardiorespiratory arrest, regained consciousness afterwards, and then developed myoclonus days or weeks after the event. Worldwide, 122 cases have been reported in the literature so far, including 1 case of Chinese. Here we report 2 Chinese LAS patients with detailed neuroimagings. Cranial single photon emission computed tomography (SPECT) of patient 1, a 52-year-old woman, showed a mild hypoperfusion in her left temporal lobe, whereas patient 2, a 54-year-old woman, manifested a mild bilateral decrease of glucose metabolism in the frontal lobes and a mild to moderate decrease of the N-acetyl aspartate (NAA) peak in the bilateral hippocampi by cranial [(18)F]-fluorodeoxyglucose positron emission tomographic (PET) scan and cranial magnetic resonance spectroscopy (MRS), respectively. We also review the literature on the neuroimaging, pathogenesis, and treatment of LAS.
慢性缺氧后肌阵挛,也称为兰斯-亚当斯综合征(LAS),是成功进行心肺复苏后的一种罕见并发症,常伴有动作性肌阵挛和小脑共济失调。它见于经历过心跳呼吸骤停、随后恢复意识、并在事件发生数天或数周后出现肌阵挛的患者。到目前为止,全球文献报道了122例,其中包括1例中国人。在此我们报告2例中国LAS患者并提供详细的神经影像学资料。患者1为一名52岁女性,其头颅单光子发射计算机断层扫描(SPECT)显示左侧颞叶轻度灌注不足;而患者2为一名54岁女性,通过头颅[(18)F]-氟脱氧葡萄糖正电子发射断层扫描(PET)和头颅磁共振波谱(MRS)分别显示额叶葡萄糖代谢轻度双侧降低以及双侧海马N-乙酰天门冬氨酸(NAA)峰轻度至中度降低。我们还回顾了关于LAS的神经影像学、发病机制及治疗的文献。