Green Kathleen J, Simpson Cory L
Department of Pathology, Northwestern University Feinberg School of Medicine, Chicago, Illinois 60611, USA.
J Invest Dermatol. 2007 Nov;127(11):2499-515. doi: 10.1038/sj.jid.5701015.
Desmosomes are highly specialized anchoring junctions that link intermediate filaments to sites of intercellular adhesion, thus facilitating the formation of a supracellular scaffolding that distributes mechanical forces throughout a tissue. These junctions are thus particularly important for maintaining the integrity of tissues that endure physical stress, such as the epidermis and myocardium. The importance of the classic mechanical functions of desmosomal constituents is underscored by pathologies reported in animal models and an ever-expanding list of human mutations that target both desmosomal cadherins and their associated cytoskeletal anchoring proteins. However, the notion that desmosomes are static structures that exist simply to glue cells together belies their susceptibility to remodeling in response to environmental cues and their important tissue-specific roles in cell behavior and signaling. Here, we review the molecular blueprint of the desmosome and models for assembling its protein components to form an adhesive interface and the desmosomal plaque. We also discuss emerging evidence of supra-adhesive roles for desmosomal proteins in regulating tissue morphogenesis and homeostasis. Finally, we highlight the dynamic nature of these adhesive organelles, examining mechanisms in health and disease for modulating adhesive strength and stability of desmosomes.
桥粒是高度特化的锚定连接,它将中间丝连接到细胞间粘附位点,从而促进形成一个超细胞支架,该支架在整个组织中分布机械力。因此,这些连接对于维持承受物理应力的组织(如表皮和心肌)的完整性尤为重要。动物模型中报道的病理学以及针对桥粒钙粘蛋白及其相关细胞骨架锚定蛋白的人类突变不断增加,突显了桥粒成分经典机械功能的重要性。然而,认为桥粒是简单地将细胞粘在一起的静态结构这一观念,掩盖了它们对环境线索作出重塑反应的易感性以及它们在细胞行为和信号传导中重要的组织特异性作用。在这里,我们回顾桥粒的分子蓝图以及组装其蛋白质成分以形成粘附界面和桥粒斑的模型。我们还讨论了桥粒蛋白在调节组织形态发生和稳态方面超粘附作用的新证据。最后,我们强调这些粘附细胞器的动态性质,研究健康和疾病状态下调节桥粒粘附强度和稳定性的机制。