Kontogiorgi Marina, Exarchos Demetrios, Charitos Christos, Floros Ioannis, Rontogianni Demetra, Roussos Charis, Routsi Christina
Department of Critical Care, Medical School of Athens University, Evangelismos Hospital, Athens Greece.
World J Surg Oncol. 2007 Oct 22;5:120. doi: 10.1186/1477-7819-5-120.
Primary cardiac neoplasms occur rarely and most of them are benign. Malignant tumors including angiosarcoma are extremely rare and have a non specific clinical presentation and a poor prognosis.
We present a case of a young male who was transferred to our hospital because of shock and multiple organ failure after a complicated pericardial biopsy. During the previous seven months he presented with recurrent episodes of pericardial effusions and tamponade. Chest computed tomography revealed a mass in the right atrium, infiltrating the myocardium and pericardium. During emergency surgery that followed, the patient died because of uncontrolled hemorrhage. Autopsy revealed the mass of the right atrium, which was identified on histological examination as primary cardiac angiosarcoma.
This case highlights the difficulties both in early diagnosis and in the management of patients with cardiac angiosarcoma.
原发性心脏肿瘤很少见，其中大多数是良性的。包括血管肉瘤在内的恶性肿瘤极为罕见，临床表现不具特异性，预后较差。
我们报告一例年轻男性病例，该患者在进行复杂的心包活检后因休克和多器官功能衰竭被转至我院。在之前的七个月里，他反复出现心包积液和心脏压塞。胸部计算机断层扫描显示右心房有一个肿块，侵犯心肌和心包。在随后的急诊手术中，患者因出血无法控制而死亡。尸检发现右心房肿块，组织学检查确定为原发性心脏血管肉瘤。
该病例凸显了心脏血管肉瘤患者早期诊断和治疗的困难。
