未分化皮脂腺癌：一种罕见的儿童癌症。

Undifferentiated sebaceous carcinoma: an unusual childhood cancer.

作者信息

Mebazaa Amel, Boussofara Lobna, Trabelsi Amel, Denguezli Mohamed, Sriha Badreddine, Belajouza Colandane, Nouira Rafia

机构信息

Department of Dermatology, Farhat Hached hospital, Sousse University, Sousse, Tunisia.

出版信息

Pediatr Dermatol. 2007 Sep-Oct;24(5):501-4. doi: 10.1111/j.1525-1470.2007.00503.x.

DOI:10.1111/j.1525-1470.2007.00503.x

PMID:17958796

Abstract

Sebaceous carcinoma is an aggressive, adnexal, rare malignant tumor that may arise in ocular or extra-ocular sites. Extraorbital sebaceous carcinoma is exceptional in childhood. We report a 12-year-old boy with an ocular sebaceous carcinoma who was first seen with an asymptomatic firm, cutaneous nodule on the right eyebrow. The tumor developed slowly within 1 year. Histologically, it was an undifferentiated sebaceous carcinoma. The patient had surgery with wide surgical margins. He was alive and free from disease at a follow-up of 34 months. Close follow-up of this tumor is recommended because of the risk of aggressive behavior.

摘要

皮脂腺癌是一种侵袭性、附属器来源的罕见恶性肿瘤，可发生于眼内或眼外部位。眶外皮脂腺癌在儿童时期极为罕见。我们报告一名12岁患有眼内皮脂腺癌的男孩，初诊时表现为右侧眉部一个无症状的实性皮肤结节。肿瘤在1年内缓慢发展。组织学检查显示为未分化皮脂腺癌。患者接受了手术切除，手术切缘广泛。随访34个月时，他存活且无疾病复发。鉴于该肿瘤有侵袭性生长的风险，建议进行密切随访。