Sato Yuichi, Matsumoto Naoya, Matsuo Shinro, Yoda Shunichi, Tani Shigemasa, Kasamaki Yuji, Takayama Tadateru, Kunimoto Satoshi, Saito Satoshi
Department of Cardiology, Nihon University School of Medicine, 1-8-13 Kanda-Surugadai, Chiyoda-ku, Tokyo, Japan.
Yonsei Med J. 2007 Oct 31;48(5):879-82. doi: 10.3349/ymj.2007.48.5.879.
Mid-ventricular obstructive hypertrophic cardiomyopathy (MVOHCM) is a rare type of cardiomyopathy, associated with apical aneurysm formation in some cases. We report a patient presenting with ventricular fibrillation, an ECG with an above normal ST segment, and elevated levels of cardiac enzymes but normal coronary arteries. Left ventriculography revealed a left ventricular obstruction without apical aneurysm. There was a significant pressure gradient between the apical and basal sites of the left ventricle. Cine magnetic resonance imaging (MRI), performed on the 10th hospital day, showed asymmetric septal hypertrophy, mid-ventricular obstruction, and an apical aneurysm with a thrombus. The first evaluation by contrast-enhanced imaging showed a subendocardial perfusion defect and delayed enhancement. It was speculated that the intraventricular pressure gradient, due to mid- ventricular obstruction, triggered myocardial infarction, which subsequently resulted in apical aneurysm formation.
心室中部梗阻性肥厚型心肌病(MVOHCM)是一种罕见的心肌病类型,部分病例与心尖部动脉瘤形成有关。我们报告一例患者,表现为心室颤动、ST段高于正常的心电图以及心肌酶水平升高,但冠状动脉正常。左心室造影显示左心室梗阻但无心尖部动脉瘤。左心室心尖部和基部之间存在显著的压力梯度。在住院第10天行电影磁共振成像(MRI)检查,显示室间隔不对称肥厚、心室中部梗阻以及伴有血栓的心尖部动脉瘤。首次对比增强成像评估显示心内膜下灌注缺损和延迟强化。推测由于心室中部梗阻导致的室内压力梯度引发心肌梗死,随后导致心尖部动脉瘤形成。