Martinez-Dominguez Pavel, Horna-Noriega Manuel, Santa-Ana-Bayona María José, Ramírez-Flores Sara, Horna-Regalado Lucia, Espinola-Zavaleta Nilda
Departamento de Cardiología Nuclear, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México. Departamento de Cardiología Nuclear Instituto Nacional de Cardiología Ignacio Chávez Ciudad de México México.
Facultad de Medicina y Ciencias Biomédicas, Universidad Autónoma de Chihuahua (UACH), Chihuahua, México. Universidad Autónoma de Chihuahua Facultad de Medicina y Ciencias Biomédicas Universidad Autónoma de Chihuahua (UACH) Chihuahua Mexico.
Arch Peru Cardiol Cir Cardiovasc. 2025 Feb 12;6(1):44-48. doi: 10.47487/apcyccv.v6i1.452. eCollection 2025 Jan-Mar.
Mid-ventricular hypertrophic cardiomyopathy is a rare subgroup within hypertrophic cardiomyopathies that may present with apical aneurysm. This condition is associated with an increased risk of cardiac adverse events, including cardiac arrest, heart failure, thromboembolic events, or sudden cardiac death. We present a case of a 41-year-old man who presented with a history of exertional dyspnea and syncope. Multimodality imaging with echocardiography and cardiac magnetic resonance showed hypertrophy of the mid-ventricular segments with apical aneurysm. An implantable cardioverter-defibrillator was implanted to prevent sudden cardiac death.
心室中部肥厚型心肌病是肥厚型心肌病中一个罕见的亚组,可能伴有心尖部动脉瘤。这种情况与心脏不良事件风险增加相关,包括心脏骤停、心力衰竭、血栓栓塞事件或心源性猝死。我们报告一例41岁男性患者,有劳力性呼吸困难和晕厥病史。超声心动图和心脏磁共振成像等多模态成像显示心室中部节段肥厚并伴有心尖部动脉瘤。植入了植入式心脏复律除颤器以预防心源性猝死。