Fukushima Hisaki, Schachern Patricia A, Cureoglu Sebahattin, Paparella Michael M
Department of Otolaryngology, University of Minnesota, Minneapolis, MN, USA.
Laryngoscope. 2008 Mar;118(3):506-7. doi: 10.1097/MLG.0b013e31815b2176.
The temporal bones of a 23-week-old female who had multiple congenital anomalies and bilateral hearing loss with trisomy 13 syndrome were evaluated under light microscopy. In the left cochlea, spiral ganglion cells and cochlear nerve fibers are absent. In the right ear, an abnormal branch of the singular nerve passes between the utricle and lateral semicircular canals and separates the two portions, one to the flattened crista of the lateral semicircular canal, the other to the utricular macula. This is a rare report describing a patient with abnormalities in three nerves, including the facial, vestibular, and cochlear nerves.
对一名患有多种先天性异常和13三体综合征伴双侧听力丧失的23周龄女性的颞骨进行了光学显微镜评估。左侧耳蜗中，螺旋神经节细胞和耳蜗神经纤维缺失。在右耳，单支神经的一个异常分支在椭圆囊和外侧半规管之间穿过，并将两者分开，一支至外侧半规管扁平嵴，另一支至椭圆囊斑。这是一篇罕见的报告，描述了一名患者的三条神经（包括面神经、前庭神经和耳蜗神经）存在异常。
