Ouakaa-Kchaou Asma, Ennaifer Rim, Belhadj Najet, Gargouri Dalila, Elloumi Hela, Romani Malika, Kochlef Asma, Kilani Afef, Kharrat Jamel, Ghorbel Abdeljabbar
Service de gastro-entérologie, Hôpital Habib Thameur, Montfleury, TN-1008 Tunis, Tunisie.
Presse Med. 2008 Feb;37(2 Pt 1):239-41. doi: 10.1016/j.lpm.2007.05.037. Epub 2007 Dec 21.
Budd-Chiari syndrome is a rare disease defined by obstruction of the hepatic portal vein. Its association with celiac disease is rare.
We report the case of a 28-year-old woman who presented with celiac disease associated with Budd-Chiari syndrome for which no cause could be found. A gluten-free diet and antivitamin K treatment led to a favorable outcome.
This case and a review of the literature suggest that the pathogenesis of these two disorders is linked.
布加综合征是一种由肝门静脉阻塞所定义的罕见疾病。其与乳糜泻的关联较为罕见。
我们报告一例28岁女性病例，该患者患有与布加综合征相关的乳糜泻，病因不明。无麸质饮食和抗维生素K治疗取得了良好效果。
该病例及文献回顾表明，这两种疾病的发病机制相关。
