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一例心室心肌致密化不全合并内脏反位及多脾畸形。

A case of noncompaction of the ventricular myocardium combined with situs ambiguous with polysplenia.

作者信息

Cho Yun-Heyong, Jin Sung Joon, Je Hyun Chul, Yoon Young-Won, Hong Bum-Kee, Kwon Hyuck Moon, Kim Tae Hoon, Rim Se-Joong

机构信息

Cardiology Division. Yondong Severance Hospital, Yonsei University College of Medicine, 146-92 Dogok-dong, Gangnam-gu, Seoul 135-720, Korea.

出版信息

Yonsei Med J. 2007 Dec 31;48(6):1052-5. doi: 10.3349/ymj.2007.48.6.1052.

DOI:10.3349/ymj.2007.48.6.1052
PMID:18159602
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2628179/
Abstract

A 33-year-old man was admitted to our hospital with chest pain and exertional dyspnea. Two-dimensional echocardiography showed prominent trabeculations and deep intertrabecular recesses, findings consistent with noncompaction of the ventricular myocardium. Thoracoabdominal CT and cardiac magnetic resonance imaging (CMR) revealed situs ambiguous with polysplenia and noncompaction of the left ventricular myocardium. CMR also demonstrated delayed enhancement of the trabeculations located at the apical portion of the left ventricle. The coronary angiogram was normal. This is the first case of noncompaction of the ventricular myocardium associated with situs ambiguous with polysplenia.

摘要

一名33岁男性因胸痛和劳力性呼吸困难入院。二维超声心动图显示显著的肌小梁和深陷的小梁间隐窝，这些表现符合心室心肌致密化不全。胸腹CT和心脏磁共振成像（CMR）显示内脏位置不明确伴多脾畸形以及左心室心肌致密化不全。CMR还显示位于左心室心尖部的肌小梁延迟强化。冠状动脉造影正常。这是首例与内脏位置不明确伴多脾畸形相关的心室心肌致密化不全病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/524b0943eb12/ymj-48-1052-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/190fd6b9cb12/ymj-48-1052-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/2f5d9099c2d8/ymj-48-1052-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/f8c06edc577e/ymj-48-1052-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/34f1cd527665/ymj-48-1052-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/524b0943eb12/ymj-48-1052-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/190fd6b9cb12/ymj-48-1052-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/2f5d9099c2d8/ymj-48-1052-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/f8c06edc577e/ymj-48-1052-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/34f1cd527665/ymj-48-1052-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/038c/2628179/524b0943eb12/ymj-48-1052-g005.jpg

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