[与乳糜泻相关的特发性门静脉高压症：1例报告]

[Idiopathic portal hypertension associated with celiac disease: one case].

作者信息

M'saddek Fehmi, Gaha Khaled, Ben Hammouda Rabie, Ben Abdelhafidh Nadia, Bougrine Fethi, Battikh Riadh, Louzir Bassem, Bouali Riadh, Bouzayane Ammar, Othmani Salah

机构信息

Service de médecine interne, Hôpital militaire de Tunis, CHU Fattouma, Bourguiba, 5000 Monastir, Tunisia.

出版信息

Gastroenterol Clin Biol. 2007 Oct;31(10):869-71. doi: 10.1016/s0399-8320(07)73981-7.

DOI:10.1016/s0399-8320(07)73981-7

PMID:18166869

Abstract

We describe for the first time a case of idiopathic portal hypertension (IPH) in a 31 year old patient with coeliac disease (CD). She had splenomegaly, pancytopenia and an unexplained portal hypertension in the absence of any histological abnormalities of the liver. The diagnosis of coeliac disease was based on histological and serological data. Treatment included a splenectomy and a splenorenal shunt.

摘要

我们首次描述了一例31岁患有乳糜泻（CD）的特发性门静脉高压（IPH）患者。她有脾肿大、全血细胞减少症，且在肝脏无任何组织学异常的情况下出现不明原因的门静脉高压。乳糜泻的诊断基于组织学和血清学数据。治疗包括脾切除术和脾肾分流术。