血红蛋白SC病婴儿的分期单心室姑息治疗

Staged single-ventricle palliation in an infant with hemoglobin SC disease.

作者信息

Law Mark A, Dreyer Zoann, Heinle Jeffrey S, Dickerson Heather A

机构信息

Department of Pediatrics, Section of Cardiology, Baylor College of Medicine and Texas Children's Hospital, Houston, Texas 77030, USA.

出版信息

Tex Heart Inst J. 2007;34(4):439-41.

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2170486/

Abstract

Staged single-ventricle palliation is used to treat many cyanotic congenital heart diseases. Hemoglobin sickle cell disease is associated with anemia and significant vascular sickling sequelae, which increase the risk associated with single-ventricle palliation. To our knowledge, there are no reports in the English-language medical literature of single-ventricle palliation having been performed on a patient who had either sickle cell anemia or sickle cell-hemoglobin C disease. Herein, we discuss our clinical and surgical management of an infant with tricuspid atresia type IA and hemoglobin sickle cell disease who survived single-ventricle palliative procedures through the 2nd stage of a bidirectional Glenn anastomosis.

摘要

分期单心室姑息治疗用于治疗多种青紫型先天性心脏病。血红蛋白镰状细胞病与贫血及严重的血管镰状化后遗症相关，这增加了单心室姑息治疗的风险。据我们所知，英文医学文献中尚无对患有镰状细胞贫血或镰状细胞-血红蛋白C病的患者进行单心室姑息治疗的报道。在此，我们讨论一名患有IA型三尖瓣闭锁和血红蛋白镰状细胞病的婴儿的临床和手术治疗情况，该婴儿通过双向格林吻合术的第二阶段单心室姑息手术存活下来。

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